Background Hereditary angioedema (HAE) resulting from C1-inhibitor deficiency is
characterized by attacks of subcutaneous and submucosal edema. Many factors have been …

BACKGROUND: C1-inhibitor (C1-INH) is a serine protease inhibitor regulating the complement,
kinin-kallikrein, coagulation, and fibrinolytic systems. Hereditary angioedema (HAE) is …

C1-inhibitor (C1-INH) is an important regulator of the complement, coagulation, fibrinolytic
and contact systems. The quantity of protease/C1-INH complexes in the blood is proportional …

Background Angioedemas localized in the upper airway are potentially life threatening, and
without proper treatment, they may lead to death by suffocation. Upper airway edemas (UAE…

Background The mechanism of idiopathic nonhistaminergic acquired angioedema (InH-AAE)
has not yet been precisely elucidated. This condition is characterized by recurrent …

Background Human fetuin A (AHSG) has been associated with the development of obesity,
insulin resistance, type 2 diabetes mellitus, and atherosclerosis. Observations on the role of …

Background Previous studies have shown association of the multifunctional hepatic protein
α2HS-glycoprotein/human fetuin A with insulin resistance, type 2 diabetes mellitus, …

Development of home treatment strategies for patients with HAE-C1-INH is an important step
toward improving the management of this debilitating condition. Studies of home-based 4 …

We wish to describe the course of pregnancies in a patient with severe hereditary angioedema
due to C1 inhibitor deficiency (HAEC1-INH). This autosomal dominant disorder belongs …

Background and aims Hereditary angioedema with C1-inhibitor deficiency (C1-INH-HAE) is
characterized by localized, non-pitting, and transient swelling of submucosal or …